Synonyms: (2R)-3-Carboxy-N,N,N-trimethyl-2-[(1-oxooctyl)oxy]-1-propanaminium inner salt; L-Carnitine octanoyl ester; C8-Carnitine
Molecular Formula: C15H29NO4
Molecular Weight: 287.4
Linear Structural Formula: C15H29NO4
Purity: >=97.0% (TLC)
Storage: 2-8C
Biochem Physiol Actions: L-Octanoylcarnitine is the physiologically active form of octanoylcarnitine and is detected in medium-chain acyl-CoA dehydrogenase (MCAD) deficiency. MCAD is characterized by intolerance to prolonged fasting, recurrent episodes of hypoglycemic coma with medium-chain dicarboxylic aciduria, impaired ketogenesis, and low plasma and tissue carnitine levels.