Synonyms: (2R)-3-Carboxy-N,N,N-trimethyl-2-(1-oxobutoxy)-1-propanaminium inner salt; Butanoyl-L-carnitine; C4-Carnitine
Molecular Formula: C11H21NO4
Molecular Weight: 231.29
Linear Structural Formula: C11H21NO4
MDL Number: MFCD01674827
Purity: >=97.0% (TLC)
Storage: 2-8C
Biochem Physiol Actions: Butyrylcarnitine is elevated in patients with Acyl-CoA dehydrogenase, short-chain (SCAD) deficiency, in infants with acute acidosis and generalized muscle weakness and in middle-aged patients with chronic myopathy localized in muscle; very long chain Acyl-CoA dehydrogenase deficiency, and celiac disease.