Synonyms: (2R)-3-Carboxy-N,N,N-trimethyl-2-(1-oxopropoxy)-1-propanaminium inner salt; L-Carnitine propionyl ester; C3-Carnitine; Propanoyl-L-carnitine
Molecular Formula: C10H19NO4
Molecular Weight: 217.26
Linear Structural Formula: C10H19NO4
MDL Number: MFCD00870024
Purity: >=94.0% (HPLC)
Storage: 2-8C
Biochem Physiol Actions: Propionylcarnitine is present in high abundance in the urine of patients with Methylmalonyl-CoA mutase (MUT) deficiency, together with Methylmalonic acid. MUT is a mitochondrial enzyme that catalyzes the isomerization of methylmalonyl-CoA to succinyl-CoA.